Sensory abnormalities in unaffected relatives in familial adult-onset dystonia.

نویسندگان

  • J P O'Dwyer
  • S O'Riordan
  • R Saunders-Pullman
  • S B Bressman
  • F Molloy
  • T Lynch
  • M Hutchinson
چکیده

Somatosensory abnormalities are found in adult-onset primary torsion dystonia (PTD). Therefore we assessed spatial discrimination thresholds (SDT), a measure of spatial acuity, in four multiplex families with adult-onset PTD. In family members aged 20 to 45 years vs controls (mean + 2.5 SD), abnormal SDTs were found in four of five affected with adult-onset PTD and in 12 of 49 unaffected relatives. Sensory abnormalities may be an endophenotype, possibly expressed later as adult-onset PTD.

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Sporadic adult onset dystonia: sensory abnormalities as an endophenotype in unaffected relatives.

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عنوان ژورنال:
  • Neurology

دوره 65 6  شماره 

صفحات  -

تاریخ انتشار 2005